Globálny slovník portálu IMED

Pojem: 
Extrakraniální radioterapie a radiochirurgie
Definícia: 

Extrakraniální stereotaktická radioterapie/radiochirurgie (SBRT – stereotactic body radiotherapy) využívá velmi přesné aplikace vysoké jednotlivé dávky záření v malém počtu frakcí. Díky stále lepší vybavenosti radioterapeutických pracovišť z hlediska možností obrazové navigace a fixace pacientů lze stereotaktický přístup využít prakticky ve všech anatomických lokalitách. S výhodou nalézá uplatnění zvláště při léčbě nádorových ložisek v plících, játrech, dutině břišní či pánvi a ve skeletu.

Kľúčové slovo: 
Radiochirurgie
Pojem: 
syndróm nedostatku testosterónu - TDS
Definícia: 

<div>TDS (testosterone deficiency syndrome) je definovan&yacute; ako klinick&yacute; a biochemick&yacute; syndr&oacute;m, ku ktor&eacute;mu doch&aacute;dza v procese starnutia mužov. Nedostatok testoster&oacute;nu u postihnut&yacute;ch mužov nepriaznivo vpl&yacute;va na funkcie viacer&yacute;ch org&aacute;nov&yacute;ch syst&eacute;mov. Vedie k podstatn&eacute;mu zhor&scaron;eniu kvality života. U mužov medzi 40 - 70 rokmi kles&aacute; biologicky akt&iacute;vny testoster&oacute;n v s&eacute;re približne o 1,2 % ročne.</div>

Pojem: 
Spolupráca endokrinológa a oftalmológa pri endokrinnej orbitopatii
Definícia: 

Práca sa venuje návodu, ako by mala vyzerať spolupráca oftalmológa s endokrinológom a zbytočným chybám, ku ktorým často zbytočne dochádza.

Kľúčové slovo: 
hrúbka extraokulárnych svalov
vnútroočný tlak
epidemiologické faktory
Endokrinná orbitopatia
farebná dopplerovská ultrasonografia
Pojem: 
Epithelial-mesenchymal transition (EMT) – epiteliálno-mezenchymálny prechod
Definícia: 

<p>
<pre>je fyziologick&yacute; proces prebiehaj&uacute;ci v embryogen&eacute;ze a pri hojen&iacute; r&aacute;n. Prejavuje sa aj v patologick&yacute;ch procesoch tumorigen&eacute;zy, ako s&uacute; inici&aacute;cia
a progresia n&aacute;dorov. Z&aacute;kladnou vlastnosťou EMT je strata epitelovej morfol&oacute;gie bunky a z&iacute;skanie vlastnost&iacute;, ktor&eacute; s&uacute; podobn&eacute; fibroblastom. Je
to sp&ocirc;soben&eacute; najm&auml; zn&iacute;ženou expresiou E-kadher&iacute;nu v d&ocirc;sledku aktiv&aacute;cie transkripčn&eacute;ho komplexu TCF/LEF s b-katen&iacute;nom, ako aj transkripčn&yacute;ch
faktorov Twist, Snai1, ZEB, ktor&yacute;ch aktivita koreluje s fenotypom kmeňov&yacute;ch buniek.</pre>
</p>

Kľúčové slovo: 
iniciácia a progresia nádorov
Pojem: 
Nasýtené mastné kyseliny (NMK)
Definícia: 

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<p class=\"MsoNormal\"><strong><span style=\"font-size: 12pt; line-height: 115%; font-family: &quot;Times New Roman&quot;,&quot;serif&quot;;\"><span></span></span></strong><span style=\"font-size: 12pt; line-height: 115%; font-family: &quot;Times New Roman&quot;,&quot;serif&quot;;\">maj&uacute; druh&yacute; najvy&scaron;&scaron;&iacute; aterog&eacute;nny potenci&aacute;l. NMK nie s&uacute; len v&nbsp;živoč&iacute;&scaron;nych tukoch (maslo 62 %, bravčov&aacute; masť 40 %), ale aj v&nbsp;niektor&yacute;ch rastlinn&yacute;ch tukoch (kokosov&yacute; a&nbsp;palmov&yacute; olej). Zatiaľ st&aacute;le ch&yacute;ba legislat&iacute;va určuj&uacute;ca povinnosť v&yacute;robcu jasne deklarovať množstvo TFMK a&nbsp;NMK v&nbsp;potravin&aacute;ch.</span></p>

Kľúčové slovo: 
aterogénny potenciál
Pojem: 
Toxokinetika
Definícia: 

<p>
cesta ortuti a&nbsp;jej zl&uacute;čen&iacute;n organizmom, od aplik&aacute;cie po elimin&aacute;ciu, je predmetom z&aacute;ujmu priemyselnej toxikol&oacute;gie. Je reprezentovan&aacute; resorpciou ortuti do organizmu, jej transportom na cieľov&eacute; miesta, biotransform&aacute;ciou a vylučovan&iacute;m z&nbsp;organizmu.&nbsp;</p>

Pojem: 
Biomonitorovanie
Definícia: 

<p>
sleduje vzťah medzi expoz&iacute;ciou ortuti a&nbsp;jej zl&uacute;čen&iacute;n a&nbsp;n&aacute;sledn&yacute;m po&scaron;koden&iacute;m zdravia.</p>

Pojem: 
neurofibrómy
Definícia: 
tumory z obalov periférnych nervov manifestujúce sa ako kožné, podkožné alebo plexiformné lézie (vznikajú zriedka pred pubertou, klinicky sú viditeľné v 30 % prípadov)
Kľúčové slovo: 
zriedkavé choroby
Pojem: 
dystusia
Definícia: 

<p>
poru&scaron;enie funkcie ka&scaron;ľov&eacute;ho reflexu, pri ktorom ka&scaron;ľov&yacute; reflex nepln&iacute; svoju &uacute;lohu ochrany a obrany d&yacute;chacieho syst&eacute;mu. To sa prejav&iacute; zv&yacute;&scaron;enou incidenciou komplik&aacute;ci&iacute; ako je napr&iacute;klad aspiračn&aacute; pneum&oacute;nia.</p>

Kľúčové slovo: 
kašľový reflex
Pojem: 
amaurosis fugax
Definícia: 

<p>
přechodn&aacute; ztr&aacute;ta zraku. Může vznikat jako jeden z př&iacute;znaků okluze v oblasti stejnostrann&eacute; vnitřn&iacute; karotidy. Je vět&scaron;. n&aacute;hl&aacute;, jednostrann&aacute;, &uacute;pln&aacute; nebo č&aacute;stečn&aacute;, trv&aacute; několik minut a může b&yacute;t prov&aacute;zena někter&yacute;mi dal&scaron;&iacute;mi př&iacute;znaky. Způsobena je uvolňov&aacute;n&iacute;m drobn&yacute;ch trombů z aterosklerotick&eacute; l&eacute;ze karotidy s embolizac&iacute; retin&aacute;ln&iacute;ch c&eacute;v nebo spasmem c&eacute;v. Může b&yacute;t tak&eacute; způsobena přechodn&yacute;m poklesem perfuze z důvodů kardiovaskul&aacute;rn&iacute;ch. Přechodn&eacute; poruchy zraku vznikaj&iacute; rovněž u někter&yacute;ch forem migr&eacute;ny.</p>

Kľúčové slovo: 
monokulární ztráta zraku
Pojem: 
myasthenia gravis
Definícia: 

<p>
nervosvalov&eacute; onemocněn&iacute;, jehož př&iacute;činou je porucha nervosvalov&eacute;ho přenosu na &uacute;rovni nervosvalov&eacute; plot&eacute;nky, kterou způsobuj&iacute; autoprotil&aacute;tky. Může se jednat o&nbsp;lokalizovanou - očn&iacute; formu nemoci nebo generalizovanou formu. Projevuje se svalovou slabost&iacute; končetin, okohybn&yacute;mi poruchami, pt&oacute;zou, dysfagi&iacute;, dysartri&iacute;, dyspno&eacute;.</p>

Kľúčové slovo: 
svalová slabost
Pojem: 
atlantoaxiální instabilita (AA instabilita)
Definícia: 

<p>
Př&iacute;činou vzniku je laxicita nebo &scaron;patn&yacute; v&yacute;vin ligament, anom&aacute;lie C2 a čast&eacute; degenerativn&iacute; změny obratlů. Vyskytuje se u 10 - 30 % pacientů s&nbsp;Downov&yacute;m syndromem, 1 &nbsp;-2 % jsou symptomatick&eacute;. D&iacute;ky AA instabilitě doch&aacute;z&iacute; k posunu C1/C2 s n&aacute;sledn&yacute;m &uacute;tlakem m&iacute;&scaron;n&iacute;ch kořenů, m&iacute;chy a možn&yacute;m rozvojem cervik&aacute;ln&iacute; myelopatie a z&nbsp;toho vypl&yacute;vaj&iacute;c&iacute; ložiskov&eacute; neurologick&eacute; symptomatiky. Může rovněž doch&aacute;zet k&nbsp; &uacute;tisku vertebr&aacute;ln&iacute; tepny s př&iacute;znaky vertebrobasil&aacute;rn&iacute; insuficience.</p>

Kľúčové slovo: 
degenerativní změny obratlů
Pojem: 
Primárna cyliárna dyskinézia (PCD)
Definícia: 

<p>
je autozom&aacute;lne reces&iacute;vne ochorenie. Patr&iacute; medzi ciliopatie, ktor&eacute; sa prejavuj&uacute; funkčn&yacute;mi zmenami a&nbsp;zmenami ultra&scaron;trukt&uacute;ry riasiniek, v&nbsp;d&ocirc;sledku čoho vznik&aacute; abnorm&aacute;lny pohyb cili&iacute; a&nbsp;n&aacute;sledn&yacute; nedostatočn&yacute; mukocili&aacute;rny transport.</p>

Kľúčové slovo: 
zriedkavé choroby
Pojem: 
ELISA (Enzyme Linked Immuno Sorbent Assay)
Definícia: 

<p>
je jednou z najpouž&iacute;vanej&scaron;&iacute;ch imunologick&yacute;ch met&oacute;d sl&uacute;žiacich k detekcii protil&aacute;tok. Met&oacute;da funguje na b&aacute;ze imunoenz&yacute;movej reakcie a využ&iacute;va dve z&aacute;kladn&eacute; vlastnost&iacute; imunoglobul&iacute;nov: schopnosť viazať sa na povrch plastu a schopnosť viazať enz&yacute;my na Fc fragmenty imunoglobul&iacute;nov&yacute;ch&nbsp; molek&uacute;l.</p>

Kľúčové slovo: 
imunologické metódy
Pojem: 
Neceliakálna negluténová enteropatia
Definícia: 

<p>
predstavuje jeden alebo viacero imunologick&yacute;ch, morfologick&yacute;ch alebo symptomatick&yacute;ch manifest&aacute;cii, ktor&eacute; s&uacute; vyvolan&eacute; glut&eacute;nom u pacientov, u ktor&yacute;ch bola vyl&uacute;čen&aacute; celiakia a in&eacute; z&aacute;palov&eacute; ochorenia čreva. Negat&iacute;vne s&uacute; s&eacute;rologick&eacute; testy na celiakiu ako aj na alergiu a&nbsp;je norm&aacute;lny histologick&yacute; n&aacute;lez. Pacienti sa klinicky zlep&scaron;ia po vyl&uacute;čen&iacute; glut&eacute;nu zo stravy.</p>

Kľúčové slovo: 
glutén

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