Globálny slovník portálu IMED

Pojem: 
Extrakraniální radioterapie a radiochirurgie
Definícia: 

Extrakraniální stereotaktická radioterapie/radiochirurgie (SBRT – stereotactic body radiotherapy) využívá velmi přesné aplikace vysoké jednotlivé dávky záření v malém počtu frakcí. Díky stále lepší vybavenosti radioterapeutických pracovišť z hlediska možností obrazové navigace a fixace pacientů lze stereotaktický přístup využít prakticky ve všech anatomických lokalitách. S výhodou nalézá uplatnění zvláště při léčbě nádorových ložisek v plících, játrech, dutině břišní či pánvi a ve skeletu.

Kľúčové slovo: 
Radiochirurgie
Pojem: 
syndróm nedostatku testosterónu - TDS
Definícia: 

<div>TDS (testosterone deficiency syndrome) je definovan&yacute; ako klinick&yacute; a biochemick&yacute; syndr&oacute;m, ku ktor&eacute;mu doch&aacute;dza v procese starnutia mužov. Nedostatok testoster&oacute;nu u postihnut&yacute;ch mužov nepriaznivo vpl&yacute;va na funkcie viacer&yacute;ch org&aacute;nov&yacute;ch syst&eacute;mov. Vedie k podstatn&eacute;mu zhor&scaron;eniu kvality života. U mužov medzi 40 - 70 rokmi kles&aacute; biologicky akt&iacute;vny testoster&oacute;n v s&eacute;re približne o 1,2 % ročne.</div>

Pojem: 
Spolupráca endokrinológa a oftalmológa pri endokrinnej orbitopatii
Definícia: 

Práca sa venuje návodu, ako by mala vyzerať spolupráca oftalmológa s endokrinológom a zbytočným chybám, ku ktorým často zbytočne dochádza.

Kľúčové slovo: 
hrúbka extraokulárnych svalov
vnútroočný tlak
epidemiologické faktory
Endokrinná orbitopatia
farebná dopplerovská ultrasonografia
Pojem: 
Epithelial-mesenchymal transition (EMT) – epiteliálno-mezenchymálny prechod
Definícia: 

<p>
<pre>je fyziologick&yacute; proces prebiehaj&uacute;ci v embryogen&eacute;ze a pri hojen&iacute; r&aacute;n. Prejavuje sa aj v patologick&yacute;ch procesoch tumorigen&eacute;zy, ako s&uacute; inici&aacute;cia
a progresia n&aacute;dorov. Z&aacute;kladnou vlastnosťou EMT je strata epitelovej morfol&oacute;gie bunky a z&iacute;skanie vlastnost&iacute;, ktor&eacute; s&uacute; podobn&eacute; fibroblastom. Je
to sp&ocirc;soben&eacute; najm&auml; zn&iacute;ženou expresiou E-kadher&iacute;nu v d&ocirc;sledku aktiv&aacute;cie transkripčn&eacute;ho komplexu TCF/LEF s b-katen&iacute;nom, ako aj transkripčn&yacute;ch
faktorov Twist, Snai1, ZEB, ktor&yacute;ch aktivita koreluje s fenotypom kmeňov&yacute;ch buniek.</pre>
</p>

Kľúčové slovo: 
iniciácia a progresia nádorov
Pojem: 
Nasýtené mastné kyseliny (NMK)
Definícia: 

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<p class=\"MsoNormal\"><strong><span style=\"font-size: 12pt; line-height: 115%; font-family: &quot;Times New Roman&quot;,&quot;serif&quot;;\"><span></span></span></strong><span style=\"font-size: 12pt; line-height: 115%; font-family: &quot;Times New Roman&quot;,&quot;serif&quot;;\">maj&uacute; druh&yacute; najvy&scaron;&scaron;&iacute; aterog&eacute;nny potenci&aacute;l. NMK nie s&uacute; len v&nbsp;živoč&iacute;&scaron;nych tukoch (maslo 62 %, bravčov&aacute; masť 40 %), ale aj v&nbsp;niektor&yacute;ch rastlinn&yacute;ch tukoch (kokosov&yacute; a&nbsp;palmov&yacute; olej). Zatiaľ st&aacute;le ch&yacute;ba legislat&iacute;va určuj&uacute;ca povinnosť v&yacute;robcu jasne deklarovať množstvo TFMK a&nbsp;NMK v&nbsp;potravin&aacute;ch.</span></p>

Kľúčové slovo: 
aterogénny potenciál
Pojem: 
Le Fort I osteotómia
Definícia: 

<div>
<span style=\"font-size: 16px\">Inc&iacute;zia sliznice nad predn&yacute;m zuborad&iacute;m so zachovan&iacute;m v&yacute;živy ďasna. Osteot&oacute;mia maxily v l&iacute;nii Le Fort I a odklopenie maxily kaud&aacute;lne. Je možn&eacute; pristupovať na zadn&uacute; stenu nazofaryngu, sfenoid&aacute;lny s&iacute;nus, klivus. Rekon&scaron;trukcia titanov&yacute;mi dl&aacute;žkami a mini-skrutkami.</span></div>
<div>
&nbsp;</div>
<div>
<span style=\"font-size: 16px\">Veľmi pravdepodobn&aacute; je po tomto pr&iacute;stupe hypest&eacute;zia druhej vetvy n. v. bilater&aacute;lne.</span></div>

Pojem: 
Mid-facial degloving
Definícia: 

<div>
<span style=\"font-size: 16px\">Inc&iacute;zia sliznice je veden&aacute; pod hornou perou, po spodine dutiny nosnej, odseparovan&iacute;m naz&aacute;lnej sliznice je možn&eacute; pristupovať na priestor od tuberculum sellae, až po horn&yacute; klivus.</span></div>

Pojem: 
Open-door maxilotómia
Definícia: 

<div>
<span style=\"font-size: 16px\">Rozsiahly, čiastočne devastačn&yacute; v&yacute;kon, s inc&iacute;ziou kože hornej pery a popod nos do oboch str&aacute;n. Po t&oacute;mii maxily v strednej vertik&aacute;lnej l&iacute;nii pomedzi zuby 11 a 21, a parci&aacute;lnej t&oacute;mii v l&iacute;nii Le Fort I. Prav&aacute; a ľav&aacute; časť maxily s&uacute; vyklopen&eacute; do str&aacute;n. Dobr&yacute; pr&iacute;stup pre gigantick&eacute; n&aacute;dory zadnej steny nazofaryngu a klivu.</span></div>

Pojem: 
Mandibulotómia
Definícia: 

<div>
<span style=\"font-size: 16px\">Devastačn&yacute;&nbsp;v&yacute;kon, inc&iacute;zia kože dolnej pery v strednej l&iacute;nii, t&oacute;mia mandibuly v strednej vertik&aacute;lnej l&iacute;nii, glossot&oacute;mia v strednej čiare a vyklopenie polov&iacute;c jazyka a mandibuly do str&aacute;n, je spojen&aacute; s vysokou mierou pooperačn&yacute;ch komplik&aacute;ci&iacute;, najm&auml; v zmysle por&uacute;ch deglutin&aacute;cie, nutnosti dlhodobej ventil&aacute;cie cez tracheostomick&uacute; kanylu a NG v&yacute;živy, pr&iacute;padne PEG, čast&yacute; je tiež v&yacute;skyt infekcie. Vysok&aacute; miera pooperačn&yacute;ch komplik&aacute;ci&iacute; v autorskom s&uacute;bore až 70 %.</span></div>

Pojem: 
Klinefelterov syndróm
Definícia: 

<p>
(XXY) je genetick&aacute; porucha sp&ocirc;soben&aacute; chromozom&aacute;lnou aneuploidiou. Postihnut&yacute; mužsk&yacute; jedinec m&aacute; namiesto jedn&eacute;ho chromoz&oacute;mu X tieto chromoz&oacute;ny dva a jeden Y. Hlavn&iacute;m n&aacute;sledkom je naru&scaron;enie v&yacute;voja semenn&iacute;kov a poruchy plodnosti, spolu s dal&scaron;&iacute;mi rysmi psychick&yacute;ch a fyzick&yacute;ch zmien. Jedinci s takouto chromozom&aacute;lnou poruchou m&ocirc;žu byť aj &uacute;plne bez pr&iacute;znakov (vč. plodnosti, ak je př&iacute;činou genetick&aacute; mozaika). 75 % mužov s XXY nevie o svojej &quot;chorobe&ldquo;, často je syndr&oacute;m diagnostikovan&yacute; až v s&uacute;vislosti s neplodnosťou, pr&iacute;padně naopak pri prenat&aacute;lnom vy&scaron;etren&iacute;. Jedn&aacute; se o druh&uacute; najčastěj&scaron;iu extrachromozom&aacute;lnu poruchu, postihnut&yacute; je jeden naroden&yacute; chlapec na 1000. Z&aacute;roveň len 90 % v&scaron;etk&yacute;ch chor&yacute;ch s pr&iacute;znakmi Klinefelterovho syndr&oacute;mu m&aacute; naozaj chromozomy XXY.</p>

Kľúčové slovo: 
chromozomálna aneupoidia
Pojem: 
Evropská síť pro surveillance legionelářské nemoci (The European Legionnaires\' Disease Surveillance Network – EWGLINET)
Definícia: 

<p>
Snahou&nbsp; evropsk&eacute;ho syst&eacute;mu&nbsp; EWGLINET&nbsp; je co nejrychleji identifikovat legionelov&eacute; epidemie mezi turisty různ&yacute;ch n&aacute;rodnost&iacute;. Syst&eacute;m se zab&yacute;v&aacute; z&aacute;chytem infekc&iacute;, morbiditou a mortalitou v&nbsp;souvislosti s&nbsp;infekcemi legionel v&nbsp;hotel&iacute;ch. Evropsk&yacute; turistick&yacute; sektor vyvinul několik iniciativ, kter&eacute; jednoznačně přispěly k&nbsp;redukci infekc&iacute; asociovan&yacute;ch s&nbsp;turismem a&nbsp;cestov&aacute;n&iacute;m.</p>

Kľúčové slovo: 
legionářská nemoc
Pojem: 
epizoocie
Definícia: 

infekční onemocnění zvířat, které se v určitém časovém období hromadně šíří. Odpovídá epidemii u lidí. Např. slintavka (stomatitis epizootica) [podle epidemie: epi-; řec. zoon zvíře]

Kľúčové slovo: 
infekční onemocnění zvířat
Pojem: 
KIR systém
Definícia: 

<p>
KIR geny a jejich produkty, tj. killer imunoglobulin-like receptory (KIR) na povrchu NK buněk jsou důležitou souč&aacute;st&iacute; vrozen&eacute; imunity člověka. NK buňky prim&aacute;rně likviduj&iacute; virem infikovan&eacute; nebo n&aacute;dorov&eacute; buňky. Tato schopnost destrukce c&iacute;lov&yacute;ch buňek je d&aacute;na vz&aacute;jemnou interakc&iacute; mezi KIR receptory a př&iacute;slu&scaron;nou specifickou HLA molekulou na povrchu buněk, neboli ligandem KIR receptorů. Genetick&aacute; diverzita KIR genů a genotypů silně připom&iacute;n&aacute; diverzitu HLA syst&eacute;mu.</p>

Kľúčové slovo: 
receptor
Pojem: 
Interferony
Definícia: 

<p>
Interferony jsou cytokiny/proteiny <a href=\"http://www.wikiskripta.eu/index.php/Nespecifick%C3%A1_imunita\" title=\"Nespecifická imunita\"><span style=\"color:windowtext;text-decoration:
none;text-underline:none\">nespecifick&eacute; imunity</span></a>, působ&iacute;c&iacute; v protivirov&eacute; obraně. Působ&iacute; parakrinně (tj. na buňky ve sv&eacute;m okol&iacute;). Reguluj&iacute; buněčnou proliferaci a&nbsp;diferenciaci. Jejich synt&eacute;za je vyvol&aacute;na patogenn&iacute;mi, <a href=\"http://cs.wikipedia.org/wiki/Rakovina\" title=\"Rakovina\"><span style=\"color:windowtext;text-decoration:none;text-underline:none\">n&aacute;dorov&yacute;mi</span></a> či mitogenn&iacute;mi podněty. Existuj&iacute; tři skupiny interferonů, přičemž v&scaron;echny interferony se do určit&eacute; m&iacute;ry pod&iacute;lej&iacute; na antivirov&eacute; odpovědi imunitn&iacute;ho syst&eacute;mu a sv&yacute;m působen&iacute;m na buňky v nich vyvol&aacute;vaj&iacute; antivirov&yacute; stav.<o:p></o:p></p>

Kľúčové slovo: 
cytokiny
Pojem: 
Argyll Robertsonův syndrom
Definícia: 

Argyll Robertsonův syndrom  – neurologický soubor příznaků, které se rozvíjejí při poškození pupilokonstrikčních a pupilodilatačních vláken v místě jejich společného průběhu horní část mezencefala a proximální konec akveduktu. Syndrom zahrnuje tyto příznaky 1. zánik přímé a konsenzuální fotoreakce 2. zachování reakce zornic na pohled do blízka 3. mióza až špendlíkové zorničky nemusí být 4. anizokorie 5. částečná dilatace zorniček na atropin. 

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